Congenital Complete Absence of Pericardium Presenting with Chest Pain: MRI Characteristics

  • Madhan Nellaiyappan Allegheny Health Network
  • Hany Demo
  • Hesham R Omar
  • Tony Fattouch
  • Orestis V Pappas
  • Devanand Mangar
  • Enrico M Camporesi

Abstract

Congenital absence of the pericardium is a very rare anomaly which has an incidence of 1 in 14000 cases in autopsy studies. Defects in the pericardium are either partial or complete with complete defects having a much benign course than partial defects. Partial defects are associated with complications like strangulation of a herniated cardiac chamber or coronary artery stenosis from external compression. Absence of the left pericardium is the most frequently encountered type of defect which accounts for 2/3 of the cases. We herein report a case of complete absence of the entire pericardium which is an extremely rare subtype with associated Cardiac magnetic resonance images.

Published
May 21, 2016
How to Cite
NELLAIYAPPAN, Madhan et al. Congenital Complete Absence of Pericardium Presenting with Chest Pain: MRI Characteristics. International Archives of Medicine, [S.l.], v. 9, may 2016. ISSN 1755-7682. Available at: <http://imed.pub/ojs/index.php/iam/article/view/1564>. Date accessed: 23 nov. 2017.
Section
Cardiology

Keywords

Pericardial absence, Cardiac MRI, congenital complete pericardial absence